Stiff Person Syndrome with Good Treatment Response to Intrathecal Baclofen
نویسندگان
چکیده
Stiff person syndrome is a rare disorder affecting the musculoskeletal system due to an underlying autoimmune process. Our case describes a 36 year old female who presented with painful, distressing, intermittent muscular rigidity and a possible associated seizure disorder. The key highlight of our case is the misdiagnosis of her disease in the early stage and the successful management of stiff person syndrome with intrathecal baclofen.
منابع مشابه
Successful intrathecal baclofen therapy for seronegative stiff-person syndrome: a case report.
We reported a 27-year-old man presenting with progressive muscle rigidity and intermittent spasms for six years. The diagnosis of stiff-person syndrome was based on the clinical features and neuroelectrophysiologic findings of continuous motor unit activities. Autoantibody against glutamic acid decarboxylase in our patient was absent either in serum or in cerebrospinal fluid. The patient was su...
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